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HEMATOLOGY
ISSN 2053-6631 Vol 4.1 • July 2016 • emjreviews.com
INSIDE
Review of
EHA 2016
Copenhagen, Denmark
CONTENTS
EDITORIAL BOARD......................................................................................................................................... 5
CONGRESS REVIEW........................................................................................................................................ 10
• Review of the 21st European Hematology Association (EHA) Annual Congress
2016, held in Copenhagen, Denmark, 9th–12th June 2016
INTERVIEWS WITH EMJ HEMATOLOGY EDITORIAL BOARD............................................................... 22
SYMPOSIUM REVIEWS
• BIOSIMILARS: SHAPING THE FUTURE IN HAEMATOLOGY............................................................. 30
HEMATOLOGY ISSN 2053-6631
CONTENTS EDITORIAL BOARD.......................
HEMATOLOGY • BRIDGING TO TRANSPLANT IN DIFFUS
Gaucher disease? He's relying on your diagnosis t
Editorial Board Editor-in-Chief: Prof Emili Mo
SUBSCRIBE TOTHEEMJ NEWSLETTER NwEwwW.newSs.eLmjEr
Welcome Welcome to this edition of our journal
Illuminating an underlying cause of haemolytic an
Foreword
10 HEMATOLOGY • July 2016
HEMATOLOGY • July 2016
12 HEMATOLOGY • July 2016
Congress Highlights GSGN-CD33A Antib
Results of Ongoing Gene Therapy Study for Haemoph
in Copenhagen, Denmark, according to a EHA press
The risk of blood cancer is a particular concern
Potential Alternative for Relapsed and Refractory
however, offers a new treatment alternative for
TKIs have significantly improved the survival rate
Despite this, cHL should still be a high priority
With promising survival outcomes and a relatively
Klaus-Michael Debatin Chairman, Department of Pa
about the long-term sequelae of our patient
our understanding of the nature of diseases
Ruben Mesa Professor of Medicine, Consultant Hem
Q: What experimental treatments are you currently
Q: What has been the proudest achievement of your
to treating thalassaemia, introducing the id
Exclusive Videos on Hematology (Clic
BIOSIMILARS: SHAPING THE FUTURE IN HAEMATOLOGY
Increasing demand for healthcare • Ageing
assess whether there are any clinically significan
The Science of Biosimilars: From Quality to Ex
and clinical data between the biosimilar and the
Reference Bio
REFERENCES 1. Baer II WH et al. Barriers to the
biopharmaceuticals. Nat Biotechnol. 2011; 29(4):3
ADVANCES IN THE TREATMENT OF NON-HODGKIN’S
of disease progression, in whom the benefits
PI3K inhibitors • Idelalisib Immune checkpoin
treatments, and is supported by clinical da
Although patients with GCB typically respond
partial response after salvage therapy achie
CC-122 Immunomodulatory effects
REFERENCES 1. Solal-Céligny P et al. F
With Newly Diagnosed Non-Germinal Center B-Cel
NEW INSIGHTS IN BONE MARROW FAILURE This sat
AA/PNH LGL
leading to apoptosis and BMF; a significant
specific marker and the diagnosis is mainly
Paroxysmal nocturnal haemoglobinuria Haemolytic
bacterial infections with antibiotics, hydration
Sci U S A. 2006;103(39):14483-8. 18. Townsley DM
Hämoglobinurie (PNH). 2015. Available view/
NAVIGATING THE CHANGING MULTIPLE MYELOMA TREAT
Exploring Recent Developments in Multiple Myel
(IGH) translocations and hyperdiploidy. Transitio
Table 1a: Phase III trials in relapsed/refractory
Table 1b: Phase III trials in relapsed/refractory
therapies. Furthermore, a meta-analysis of triple
treatment should continue until progressi
immunomodulatory drugs, histone deacetylase
was similar to that seen in the overall p
Annual Meeting, 9-12 June 2016. 34. San-Miguel
Phase 2 Study of the All-Oral Combination of Inv
Abstract Reviews EVIDENCE-BASED TRANSFUSION MEDIC
EHA 2016 in a given patient for a given procedur
Abstract Reviews with lower limb SVT not involvi
EHA 2016 GBT440 treatment compared with
Abstract Reviews (mutant JAK2, MPL or CALR, or t
EHA 2016 FAMILY-DIRECTED CORD BLOOD BANKIN
Abstract Reviews RESULTS A total of 338 directed
EHA 2016 conservative approximation of progre
Abstract Reviews function, whilst others h
EHA 2016 CHRONIC LYMHOCYTIC LEUKAEMIA: TREATMEN
Abstract Reviews 370(12):1101-10. 9. Hillmen P
EMJ EUROPEAN MEDICAL
EDITOR’S PICK Dire
INTRODUCTION Bleeding events have been r
Bioavailability If DE capsules are opened, t
Table 1 continued. Dabigatran Rivaroxaban
Table 1 continued. PE: pulmonary embolism; THR:
any other anticoagulant is strictly contraindicat
Table 2 continued. Dabigatran P-gp substrate
Table 2 continued. Dabigatran P-gp substrate
http:/www.fda.gov) clearly suggest an association
Table 3 continued. Indication Emergent situation†
with LMWH or UFH, especially for patients with hi
Intern Med. 2015;175(1):18-24. 9. Russo V et al.
(Randomized Evaluation of Long-Term Anticoagul
BRIDGING TO TRANSPLANT IN DIFFUSE LA
option is to initiate high-dose therapy pri
1.0 0.8 0.6 0.4 Survival probability 0.2 0.
in patients with refractory DLBCL repor
Table 1: Overall survival according to prognostic
Table 2: Response rates until the end of study in
p=0.005; HR: 0.6 [95% CI: 0.42–0.86]). Simi
REFERENCES 1. International Agency for Research
after high-dose therapy and autologous transplant
THROMBOCYTOPENIA CAUSED BY INHERITED HA
a platform for the discovery of new genetic defec
Runt-Related Transcription Factor 1 The core bind
Gene references Platelet disorder OMIM entry
counts have been documented in a number of family
caused by mutations affecting the DNA binding fac
of defective secretion of dense granules on
Ecotropic Viral Integration Site 1 The MECOM ge
develop myeloid malignancies to human chromosome
ANKRD26 regulatory region induce MAPK hype
THE RELATIVE CONTRIBUTIONS OF GERMLINE VARI
in leukaemia. The inability to account for paedia
abundant somatic mutation. Well known instability
Genome-wide association studies have identified he
the largest absolute number of variants were in t
paediatric cancer. While targeting developmental
pediatric and hematologic cancers: a moving t
CURRENT MANAGEMENT OF ADULT ACUTE LYMPHOBLASTIC
molecular targets and newly developed therapies,
Minimal Residual Disease MRD is the detection
Results appeared significantly better when
negativity was reached in 50–83% of cases and a
a nutrient sensor and regulator of translation in
not benefit sufficiently from imatinib, and in who
‘acute myeloid leukaemia-like’ chemother
without allogeneic SCT. Furthermore, it has been
20. Mohty M et al. Reduced intensity conditioning
complete remissions in adults with relaps
like acute lymphoblastic leukemia. Blood. 2012;12
MANAGEMENT OF CHILDREN WITH SICKLE CELL DISEASE I
Europe and identifying the greatest unmet clinica
MANAGEMENT OF SICKLE CELL DISEASE IN CHILDHOOD AN
SCD, not only in research studies but also
Currently, a study is underway to determine the l
in the 21st century: incidence, diagnosis and hee
insufficiency. Ann Hematol. 2004;83(1): 18-21. 51
UPCOMING EVENTS 18th Meeting of the European Asso
HEMATOLOGY 10th Anniversary Conference Academy fo
EUROPEAN MEDICAL JOURNAL provides influential arti
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